How not to miss Kaposiform haemangioendothelioma in neonates?: MRI findings
Kaposiform haemangioendothelioma with Kasabach–Merritt phenomenon
A 2 months old termed baby boy presented to casualty with rapid breathing and interrupted feeding for 2 weeks. There was no history of documented fever, trauma or foreign body ingestion. He was delivered via spontaneous vaginal delivery to non-consanguineous parents. He was diagnosed to have right lower limb and right scrotal haemangioma since birth. The abdomen was distended with hemihypertrophy of the right lower limb (conventional radiograph). He was noted to have bruises along the right side of the abdomen and right lower limb that had worsened in parallel with the onset of his illness. At the time of presentation, he had a severe uncompensated coagulopathy. Physical examination noted violaceous discoloration of the abdomen and right leg with dilated vessels visible in his abdominal wall. Magnetic resonance images (MRI) revealed a large right sided mass with ill-defined borders that permeated through the surrounding fat tissue extending from the right side of the trunk to the right lower limb, consistent with a Kaposiform haemangioendothelioma.